Article Figures & Data
Figures
- Fig 1.
Transabdominal sonogram obtained in a fetus with ACC and DWM at 27 weeks’ gestation. Coronal view shows elevation of the third ventricle, vertical orientation of the frontal horns (arrows), and absence of the corpus callosum.
- Fig 2.
Single-shot half-Fourier turbo spin-echo MR images of the fetal brain at 27 weeks’ gestation. Coronal (A) and axial (B) images demonstrate agenesis of the corpus callosum and absence of any frontal cyst.
- Fig 3.
Neonatal brain MR image taken when the patient was 1 day old. Axial T1-weighted image (similar plane to that of Figure 2B) shows the increased size of the frontal and occipital horns (compare with prenatal scan) in addition to the new finding of a frontal para-midline cyst (C).
- Fig 4.
Neonatal cranial sonogram obtained when the patient was 5 days old. Coronal view in plane similar to that of Figures 2B and 3 demonstrates agenesis of the corpus callosum. In addition, a large frontal paramidline cyst is present (C).
Tables
Classification of agenesis of the corpus callosum with interhemispheric cyst after Barkovich et al (3)
Type 1* Subtype Cyst Characteristics Communication Associated Abnormalities Type 1a: Presumed communicating hydrocephalus Isointense to CSF (MR), unilocular Communication with lateral ventricles only Macrocephaly, hydrocephalus, Dandy-Walker malformation Type 1b: Hydrocephalus secondary to diencephalic anomaly Isointense to CSF (MR), unilocular Communication with and obstruction of third ventricle Macrocephaly, diencephalic malformation (eg, thalamic fusion without subcortical heterotopia) Type 1c: Small head size and cerebral hypoplasia Isointense to CSF (MR), unilocular Communication with lateral and third ventricles Microcephaly, cerebral dysplasia or hypoplasia Type 2† Type 2a: No abnormality apart from ACC Isointense to CSF (MR), multilocular No communication with lateral or third ventricles Macrocephaly, hydrocephalus Type 2b: Aicardi syndrome Hyperattenuation (CT), hyperintense (T1W MR), multilocular No communication with lateral or third ventricles Female predominance, subependymal heterotopia, polymicrogyria, seizures, hypoplastic falx cerebri, uni- or bilateral ventriculomegaly, developmental delay Type 2c: Subcortical heterotopia Isointense to CSF (MR), multilocular No communication with lateral or third ventricles Subcortical heterotopia, developmental delay * Extension or diverticulation of third or lateral ventricles.
† Loculated, lack of communication with ventricular system.
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