RT Journal Article
SR Electronic
T1 Remote Vascular Catastrophes after Neurovascular Interventional Therapy for Type 4 Ehlers-Danlos Syndrome
JF American Journal of Neuroradiology
JO Am. J. Neuroradiol.
FD American Society of Neuroradiology
SP 974
OP 976
VO 21
IS 5
A1 Horowitz, Michael B.
A1 Purdy, Phillip D.
A1 Valentine, R. James
A1 Morrill, Kevin
YR 2000
UL http://www.ajnr.org/content/21/5/974.abstract
AB Summary: Type 4 Ehlers-Danlos Syndrome (EDS 4) is the most malignant form of Ehlers-Danlos Syndrome, often accompanied by neurovasacular complications secondary to vessel dissection or aneurysms. The fragile nature of connective tissue in these patients makes exovascular and endovascular treatment hazardous. We have treated four patients with EDS 4 over the last 8 years by using neuroendovascular procedures. Two of these individuals suffered remote vascular injuries around the time of their procedures and ultimately died. The circumstances surrounding their deaths will make up the body of this report.